It’s like being trapped under water

A man sentenced to death by the King was granted a reprieve of one year. He discovered that the King was a lover of horses and promised that within a year he would teach the King’s horse to fly. His friends laughed at him. But the man explained, “Within a year the King may die, or the horse may die, or I may die. Besides, who knows? The King’s horse may learn to fly”. I recently told this story of hope to a friend who was becoming increasingly incapacitated by idiopathic pulmonary fibrosis (IPF), a disease with no known cure.

IPF is the most common interstitial lung disease (ILD), a group of diseases affecting the tissue and space around the air sacs in the lungs. These diseases are more rare that asthma, chronic obstructive lung disease or even lung cancer, but they are severe and very life-limiting. Yet most people and some doctors have never heard of this problem.

I never suspected that my tennis partner had idiopathic pulmonary fibrosis.

But in recent years it became apparent that something was wrong. He developed a dry hacking cough, chest discomfort, progressive shortness of breath, fatigue and weakness.

This happens because IPF causes extensive, progressive, scarring of lung tissue. The alveoli (air sacs) in the lungs stiffen and become thick, decreasing the amount of oxygen in the blood stream. In effect, IPF is a slow strangulation of the body’s oxygen supply, essential for life. My friend remarked, “It takes hours to do anything. It’s like being trapped under water and trying to surface for air.”

As the disease progresses and the amount of functioning lung tissue diminishes, other problems make life increasingly difficult. Pressure may build up in pulmonary arteries putting excess strain on the heart, which, in turn, begins to fail.

In many cases doctors cannot pin-point a cause for ILD. But in others the cause is obvious. When miners inhale coal dust or asbestos for instance. Others develop scarring of the lung by working long hours sand blasting or bird farming. There is also a condition called hypersensitivity pneumonitis often due to inhaling dust contaminated with bacterial, fungal or animal products.

Smoking makes the illness worse. In addition, some connective tissue diseases such as rheumatoid arthritis, scleroderma, sarcoidosis and radiation therapy to the chest cause lung scarring. As readers know I have repeatedly warned about the dangers of excessive and often needless radiation therapy.

The diagnosis of pulmonary fibrosis is made by lung doctors using lung function tests, high-resolution CAT scans of the chest and/or a lung biopsy. The pathologist can confirm the presence of scarring.

Unfortunately there are no approved treatments for IPF except for double lung transplant. In the past doctors used a combination of prednisone and azathioprine with an antioxidant (NAC) to treat IPF. Recently, however this approach was found to be much more harmful than placebo and is no longer recommended. That’s why it’s so important for patients to taker charge of their own lives. This means trying to avoid infection and making sure they are vaccinated against pneumonia.

Knowing you have an incurable disease with just a few years to live is never easy to accept. Patients desperately hope the diagnosis is wrong and often frantically search the Internet looking for a cure. And the more they delve into IPF the more confused they become, particularly when no apparent cause for the scarring can be found.

The average length of life from the time of IPF diagnosis is two to five years. But the course of the disease varies from patient to patient. For some its course is rapid and for others a slow gradual one. Fortunately fate can be kind as some patients have lived as long as 20 years.

What about the future? Recently the Canadian Pulmonary Fibrosis Foundation, along with a team of researchers at the University of Toronto, is exploring the use of new anti-scarring therapies in fighting this disease. There is always hope. Those inflicted with IPF may live to see that the King’s horse has learned to fly.

See the web site at For comments, go to

Just Posted

Pursuit with rogue semi ends in arrest

RCMP chased a stolen semi tractor from Red Deer to Airdrie

Red Deer College students host event for survivors of sexual assault

Take Back the Night aims to ‘shatter the silence and stop the violence’

City responds to this year’s provincial budget

Local health and social infrastructure needs not met, officials say

University of Calgary and RDC partner for new collaborative degree

Bachelor of Science in Psychology program launches in Red Deer

Bard on Bower will travel to more Red Deer parks

Prime Stock finishing casting for Romeo & Juliet, Henry V and A Midsummer Night’s Dream

WATCH: Student for a Day at Red Deer College

A video tour of the fine arts department

Canadian cities hold March for our Lives events in wake of Florida shooting

Hundreds of people support the massive March for Our Lives event in Washington, D.C.

Embattled band Hedley plays last show before hiatus

About 3,000 tickets had sold for final performance at B.C. venue

Canada’s Kaetlyn Osmond wins figure skating world title

The 22-year-old fwon the women’s singles crown with her Black Swan routine

Calgary police investigate man posing as Calgary firefighter

Calgary police are looking for information on a suspect who stole a firefighter’s ID

Alberta tells B.C. to stop opposing pipelines if it doesn’t like gas prices

John Horgan said he would like to see the federal government step in to deal with high gas prices.

Uber self-driving crash video calls safety, rules into question

Experts say footage shows that vehicle’s sensors should have spotted pedestrian, initiated braking

Bashaw RCMP arrest man wanted in several crimes

Variety of criminal charges, including vehicle theft, facing-29-year-old man caught in Alix

Valuable rings stolen out of car in Thorsby Mar. 22

Thorsby/Breton RCMP seek to recover special stolen items

Most Read